Syndromatic pulmonary lymphangioleiomyomatosis

Lymphangioleiomyomatosis tuberous sclerosis cutaneous angiofibromas Shagreen's patches Koenen's tumors

Authors

  • Cristhian Velásquez
    crismaodm.cc@gmail.com
    Departamento de Radiología e imágenes Diagnosticas, Hospital Regional de Occidente, Quetzaltenango, Guatemala., Guatemala
  • José Echeverría Departamento de Radiología e imágenes Diagnosticas, Hospital Regional de Occidente, Quetzaltenango, Guatemala., Guatemala
  • Mary Cotí Departamento de Radiología e imágenes Diagnosticas, Hospital Regional de Occidente, Quetzaltenango, Guatemala., Guatemala
April 21, 2022
September 15, 2022

Lymphangioleiomyomatosis (LAM) is a rare disease that predominantly affects women, especially those of childbearing age. It occurs sporadically or is associated with tuberous sclerosis complex. The case of a 25-year-old female patient is presented,

How to Cite

Syndromatic pulmonary lymphangioleiomyomatosis. (2022). Revista médica (Colegio De Médicos Y Cirujanos De Guatemala), 161(3), 268-270. https://doi.org/10.36109/rmg.v161i3.504